A Child with Crouzon’s Syndrome and Ventricular Septal Defect Posted for Ventriculoperitoneal Shunt Surgery

Authors

  •   Aastha Srivastava Department of Anaesthesia, Anaesthesia and Pain Management, Himalayan Institute of Medical Sciences, SRHU, Swami Ram Nagar, Dehradun, Uttarakhand
  •   Parul Jindal Department of Anaesthesia, Anaesthesia and Pain Management, Himalayan Institute of Medical Sciences, SRHU, Swami Ram Nagar, Dehradun, Uttarakhand
  •   Yashwant S. Payal Department of Anaesthesia, Anaesthesia and Pain Management, Himalayan Institute of Medical Sciences, SRHU, Swami Ram Nagar, Dehradun, Uttarakhand
  •   Shreesh Malhotra Department of Anaesthesia, Anaesthesia and Pain Management, Himalayan Institute of Medical Sciences, SRHU, Swami Ram Nagar, Dehradun, Uttarakhand

Keywords:

Congenital heart disease, crouzonal syndrome, hydrocephalus, ventriculoperitoneal shunt

Abstract

Quite often in our anaesthesia practice, we encounter syndromic children presenting to us for surgery either for correction of the primary deformity or for a secondary problem. A child with a craniofacial syndrome presents with a number of issues for the anaesthetist, with difficult airway being one of the most important one. The challenge increases with increasing complexity of the surgery. When pre‑anaesthetic evaluation of such a child is done, other congenital anomalies also might come into picture. These may include various types of congenital malformations or congenital heart diseases which may be diagnosed incidentally while evaluation. Anaesthetic management of such a child presenting for surgery includes a thorough pre‑anaesthetic evaluation, formulating a plan for intraoperative anaesthetic management and proper postoperative care. This case report describes a child with Crouzon’s syndrome posted for ventriculoperitoneal shunt surgery.

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Published

2017-04-01

How to Cite

Srivastava, A., Jindal, P., Payal, Y. S., & Malhotra, S. (2017). A Child with Crouzon’s Syndrome and Ventricular Septal Defect Posted for Ventriculoperitoneal Shunt Surgery. Karnataka Anaesthesia Journal, 3(2), 34–36. Retrieved from http://karnatakaanesthesiajournal.in/index.php/kaj/article/view/138924

Issue

Volume 3, Issue 2, April-June 2017

Section

Case Reports

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