Morquio Syndrome with Acute Cord Compression: An Anesthetic Challenge

Authors

  •   Nischala Dixit Department of Anesthesia and Critical Care, St John’s Medical College and Hospital, Bengaluru, Karnataka
  •   Bindu George Department of Anesthesia and Critical Care, St John’s Medical College and Hospital, Bengaluru, Karnataka
  •   M. Manjuladevi Department of Anesthesia and Critical Care, St John’s Medical College and Hospital, Bengaluru, Karnataka
  •   Vineesh K. Varghese Department of Anesthesia and Critical Care, St John’s Medical College and Hospital, Bengaluru, Karnataka
  •   Archana Kalaichelvam Department of Anesthesia and Critical Care, St John’s Medical College and Hospital, Bengaluru, Karnataka

Keywords:

Airway management, Morquio syndrome, spinal cord compression

Abstract

Morquio syndrome with skeletal and extraskeletal manifestations is an anesthetic challenge. Airway management in children with Morquio syndrome can pose added risks of atlantoaxial instability, spinal cord compression, and distorted airway anatomy, leading to difficult mask ventilation and intubation. We report the anesthetic management of a 4‑year‑old child with Morquio syndrome who presented with acute cord compression and underwent emergency decompression of the stenotic spinal canal at the craniovertebral junction. Thorough preoperative evaluation, meticulous planning, and vigilant monitoring in the perioperative period are essential for safe anesthetic management.

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Published

2015-07-01

How to Cite

Dixit, N., George, B., Manjuladevi, M., Varghese, V. K., & Kalaichelvam, A. (2015). Morquio Syndrome with Acute Cord Compression: An Anesthetic Challenge. Karnataka Anaesthesia Journal, 1(3), 143–145. Retrieved from http://karnatakaanesthesiajournal.in/index.php/kaj/article/view/139380

Issue

Volume 1, Issue 3, July- September 2015

Section

Case Reports

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