Anaesthetic Management of Kartageners Syndrome Posted for Kasai Surgery

Authors

  •   Saraswathi Nagapaa Department of Anesthesia, Bangalore Medical College and Research Institute, Bengaluru - 560002, Karnataka
  •   Sandhya Kalappa Department of Anesthesia, Bangalore Medical College and Research Institute, Bengaluru - 560002, Karnataka

DOI:

https://doi.org/10.4103/kaj/2020/v18i1-2/159365

Keywords:

Anesthesia, Biliary Atresia, Hepatobiliary Surgery, Situs Inversus Totalis

Abstract

Kartagener's syndrome is a rare autosomal recessive disorder presenting with a triad of sinusitis, bronchicetasis and situs inversus with dextrocardia. It occurs in 50% of patients with situs inversus .Patients with genetic disorders associated with multiple congenital anomalies present unique challenges to the anesthesiologist. We report the successful intraoperative management of a child with biliary atresia, situs inversus totalis, and Kartegener syndrome scheduled for corrective biliary surgery. We recommend that patients with multiple congenital anomalies need to be thoroughly and cautiously evaluated.

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Published

2020-06-04

How to Cite

Nagapaa, S., & Kalappa, S. (2020). Anaesthetic Management of Kartageners Syndrome Posted for Kasai Surgery. Karnataka Anaesthesia Journal, 18(1-2), 37–40. https://doi.org/10.4103/kaj/2020/v18i1-2/159365

Issue

Volume 18, Issue 1-2, January-June 2020

Section

Case Reports
Crossref
Scopus
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Europe PMC

References

Losa M, Ghelfi D, Hof E, Fanconi S, Helix H. Kartagener syndrome: An uncommon cause of neonatal respiratory distress? Eur J Paediatr, 1995; 154:236-238. https://doi.org/10.1007/BF01954280. PMid:7758526.

Chuhwak EK. Kartagener syndrome in a Nigerian African−A case report and literature review. Niger J Med, 2009; 18(4):424-427. PMID: 20120152. https://doi.org/10.4314/njm.v18i4.51258. PMid:20120152.

O’Callaghan C, Chetcuti P, Moya E. High prevalence of primary ciliary dyskinesia in a British Asian population. Arch Dis Child, 2010; 95(1):51-52. Epub. 2009 Aug 30. PMID: 19720631. https://doi.org/10.1136/adc.2009.158493. PMid:19720631.

Burduk P, Wawrzyniak, K, Kaźmierczak W, Kusza K. Kartagener’s syndrome - anaesthetic considerations for ENT surgery. Otolaryngologia polska. The Polish otolaryngology, 2012; 66:291-294. https://doi.org/10.1016/j.otpol.2012.05.020.

Garg R, Goila A, Sood R, Pawar M, Borthakur B. Perioperative anesthetic management of a patient with biliary atresia, situs inversus totalis, and kartegener syndrome for hepatobiliary surgery. J Anaesthesiol Clin Pharmacol, 2011; 27(2):256-258. https://doi.org/10.4103/0970-9185.81837. PMid: 21772694 PMCid:PMC3127313.

Bajwa SS, Kulshrestha A, Kaur J, Gupta S, Singh A Amarjit, Parmar SS. The challenging aspects and successful anaesthetic management in a case of situs inversus totalis. Indian Journal of Anaesthesia, 2012; 56(3):295-297. https://doi.org/10.4103/0019-5049.98781. PMid:22923832 PMCid:PMC3425293.

Ul Hassan A, Hassan G, Khan SH, Rasool Z, Abida A. Ciliopathy with special emphasis on Kartageners syndrome. Int J Health Sci (Qassim), 2009; 3(1):65-69.