Lamellar Ichthyosis; An Uncommon Acquaintance with Anesthesiologists: Overcoming Barriers

Authors

  •   Ravi Narayanan Department of Anaesthesiology, Sparsh Hospital, Bengaluru, Karnataka
  •   Sharanu Patil Department of Anaesthesiology, Sparsh Hospital, Bengaluru, Karnataka
  •   Raghuvarathan Department of Anaesthesiology, Sparsh Hospital, Bengaluru, Karnataka

Keywords:

Hyperkeratosis, lamellar ichthyosis, skin scaling

Abstract

Lamellar ichthyosis constitutes a distinct group of inherited ichthyosis characterized by excessive scaling and dryness. Abnormalities in epidermal differentiation and metabolism contribute to excessive keratinization, which is a hallmark of this disorder. We present here the successful anesthetic management of a 13‑year‑old boy with lamellar ichthyosis for the correction of Genu Valgum deformity.

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Published

2017-01-01

How to Cite

Narayanan, R., Patil, S., & Raghuvarathan. (2017). Lamellar Ichthyosis; An Uncommon Acquaintance with Anesthesiologists: Overcoming Barriers. Karnataka Anaesthesia Journal, 3(1), 6–9. Retrieved from https://karnatakaanesthesiajournal.in/index.php/kaj/article/view/138918

Issue

Section

Case Reports

References

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