A Case of Epidermolysis Bullosa Posted for Contracture Release and External Fixator Application of Hand under General Anaesthesia
DOI:
https://doi.org/10.4103/kaj/2018/v16i3-4/143682Keywords:
Airway, Anaesthesia, Epidermolysis Bullosa, SkinAbstract
Epidermolysis bullosa is a rare autosomal inherited disorder involving skin and mucous membrane, and characterized by blister and bullae formation all over the body. Meticulous attention needs to be given during perioperative period to ensure that no new bullae are formed and the existing ones are not disturbed. We present successful management of a case who presented for multiple procedures at different time intervals.Downloads
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